Retroperitoneal fibrosis

CT · MRI

First and second year — the floor first, then every step

A periaortic soft-tissue mantle at L4–L5 that encases the aorta and draws the ureters medially — separate idiopathic or IgG4-related fibrosis from lymphoma and malignant fibrosis, and report the ureteric obstruction.

Orient first

  • Most are idiopathic or IgG4-related; secondary causes include drugs, radiotherapy and malignancy.
  • Fibrosis does not displace the aorta anteriorly from the spine, whereas lymphoma and metastatic nodes often lift it.
  • Medial deviation of the middle third of the ureters with hydronephrosis is typical.

Acquire the study

  • Portal venous phase CT abdomen-pelvis with coronal reformats.

The manoeuvre

  • Periaortic soft-tissue mantle below the renal arteries; its thickness in mm and craniocaudal extent.
  • Is the aorta lifted off the spine? (favours lymphoma/metastasis).
  • Ureters: medial deviation, hydronephrosis, level of obstruction.
  • IVC compression; other IgG4 organs (pancreas, kidneys, bile ducts).

What confirms it

  • A periaortic mantle with medial ureteric deviation and no nodal mass; biopsy when atypical.

What licenses you to exclude it

  • A normal periaortic fat plane excludes retroperitoneal fibrosis.

The classic misread

  • Calling an inflammatory abdominal aortic aneurysm fibrosis — measure the aortic diameter.

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