Left ventricular hypertrabeculation ("non-compaction")

MRI

First and second year — the floor first, then every step

Excess trabeculation is common and often benign (athletes, pregnancy, sickle cell); the diagnosis of a cardiomyopathy needs more than a ratio — LV dilatation or dysfunction, LGE, thin compacted myocardium, and family history.

Orient first

  • The Petersen ratio (non-compacted/compacted > 2.3 in end-diastole — verify) is sensitive but not specific.
  • Current thinking treats hypertrabeculation as a phenotype that may accompany other cardiomyopathies.
  • Complications: heart failure, arrhythmia, thromboembolism (LV thrombus).

Acquire the study

  • CMR: cine SSFP short-axis stack and long axes; LGE; native T1 if available.

The manoeuvre

  • End-diastolic long-axis cine: maximal non-compacted/compacted ratio in the segment with the most trabeculation.
  • Compacted myocardium thickness in mm.
  • LV volumes and EF indexed to BSA.
  • LGE: presence and pattern (adverse prognosis).
  • LV thrombus on LGE with a long inversion time.

What confirms it

  • Hypertrabeculation with LV dilatation/dysfunction, LGE or a family history — a cardiomyopathy phenotype.

What licenses you to exclude it

  • Isolated hypertrabeculation with normal size, function and no LGE should be reported as a trait, not a disease.

The classic misread

  • Labelling a healthy athlete with non-compaction cardiomyopathy.

More searches

More in Cardiac and vascular